Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center For Human Genetics And Laboratory Diagnostics, |
RCV001801314 | SCV002047523 | likely pathogenic | Thrombophilia due to protein C deficiency, autosomal dominant | 2021-08-04 | criteria provided, single submitter | clinical testing | |
Gene |
RCV003318690 | SCV004022952 | uncertain significance | not provided | 2023-01-25 | criteria provided, single submitter | clinical testing | Reported in the heterozygous state in individuals with protein C deficiency (Alhenc-Gelas et al., 2020); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 32717757) |