Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001380840 | SCV001579025 | pathogenic | Thrombophilia due to protein S deficiency, autosomal recessive | 2020-02-17 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals with PROS1-related conditions. Loss-of-function variants in PROS1 are known to be pathogenic (PMID: 9241758). For these reasons, this variant has been classified as Pathogenic. This sequence change creates a premature translational stop signal (p.Gln362*) in the PROS1 gene. It is expected to result in an absent or disrupted protein product. |