Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000219850 | SCV000273348 | pathogenic | Hereditary cancer-predisposing syndrome | 2015-01-02 | criteria provided, single submitter | clinical testing | The c.458_461delATTT pathogenic mutation, located in coding exon 5 of the PTEN gene, results from a deletion of 4 nucleotides at positions 458 through 461, causing a translational frameshift with a predicted alternate stop codon. Since frameshifts are typically deleterious in nature, this alteration is interpreted as a disease-causing mutation (ACMG Recommendations for Standards for Interpretation and Reporting of Sequence Variations. Revision 2007. Genet Med. 2008;10:294). |