Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000491839 | SCV000579989 | pathogenic | Hereditary cancer-predisposing syndrome | 2015-05-14 | criteria provided, single submitter | clinical testing | The c.512_515delAGAG pathogenic mutation, located in exon 6 of the PTEN gene, results from a deletion of 4 nucleotides between positions 512 and 515, causing a translational frameshift with a predicted alternate stop codon. Since frameshifts are typically deleterious in nature, this mutation is interpreted as disease-causing (ACMG Recommendations for Standards for Interpretation and Reporting of Sequence Variations. Revision 2007. Genet Med 2008;10:294). |