Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002396759 | SCV002697182 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-06-20 | criteria provided, single submitter | clinical testing | The p.A488T variant (also known as c.1462G>A), located in coding exon 16 of the RB1 gene, results from a G to A substitution at nucleotide position 1462. The alanine at codon 488 is replaced by threonine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Center for Genomic Medicine, |
RCV003493944 | SCV004242592 | uncertain significance | not specified | 2024-02-06 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV004007322 | SCV004817974 | uncertain significance | Retinoblastoma | 2023-03-04 | criteria provided, single submitter | clinical testing |