Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000709349 | SCV000838927 | uncertain significance | Retinoblastoma | 2018-07-02 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002458329 | SCV002736741 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-02-05 | criteria provided, single submitter | clinical testing | The p.K814R variant (also known as c.2441A>G), located in coding exon 23 of the RB1 gene, results from an A to G substitution at nucleotide position 2441. The lysine at codon 814 is replaced by arginine, an amino acid with highly similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |