Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Sing |
RCV005235864 | SCV005881518 | likely pathogenic | Patterned macular dystrophy 1 | 2025-02-05 | criteria provided, single submitter | clinical testing | Variant is not found in gnomAD exomes or genomes (PM2). REVEL score is 0.879 (PP3_mod). Other variants on this amino acid residue are classified as pathogenic (c.422A>G, c.421T>G, c.421T>C, PM5). Variant is located ina mutational hotspot where >50% of variants are pathogenic (PM1) |