Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001873755 | SCV002232591 | pathogenic | PRPH2-related disorder | 2023-07-03 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 1175260). This premature translational stop signal has been observed in individual(s) with clinical features of PRPH2-related conditions (PMID: 29555955). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Glu191*) in the PRPH2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in PRPH2 are known to be pathogenic (PMID: 8111389, 8485575, 8485576, 8675410, 16916875, 17504850, 22863181, 25675413, 26061163, 27365499, 29555955, 33546218). |
Institute of Human Genetics, |
RCV004815555 | SCV005072557 | pathogenic | Retinal dystrophy | 2020-01-01 | criteria provided, single submitter | clinical testing | |
Leiden Open Variation Database | RCV001530308 | SCV001745077 | pathogenic | not provided | 2021-04-06 | no assertion criteria provided | curation | Curator: Global Variome, with Curator vacancy. Submitters to LOVD: LOVD, Manon Peeters. |