Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001940505 | SCV002192264 | uncertain significance | PRPH2-related disorder | 2021-05-06 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine with glycine at codon 251 of the PRPH2 protein (p.Arg251Gly). The arginine residue is highly conserved and there is a moderate physicochemical difference between arginine and glycine. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt PRPH2 protein function. This variant has not been reported in the literature in individuals with PRPH2-related conditions. This variant is present in population databases (rs772701367, ExAC 0.01%). |
Ambry Genetics | RCV002557794 | SCV003622797 | uncertain significance | Inborn genetic diseases | 2022-06-03 | criteria provided, single submitter | clinical testing | The c.751A>G (p.R251G) alteration is located in exon 2 (coding exon 2) of the PRPH2 gene. This alteration results from a A to G substitution at nucleotide position 751, causing the arginine (R) at amino acid position 251 to be replaced by a glycine (G). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |