Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
NEI Ophthalmic Genomics Laboratory, |
RCV001250364 | SCV001424692 | uncertain significance | Cone-rod dystrophy | 2020-01-07 | criteria provided, single submitter | clinical testing | The variant NM_000322.4:c.937C>T in the PRPH2 gene has not been reported to our knowledge . We found this variant in 1 patient(s) in a PRPH2 cohort study (Reeves et al. 2020). This variant is listed in dbSNP and/or HGMD (rs746742888). It is present in gnomAD browser (AF 0.0000203). This variant is not already listed in ClinVar. It is not enriched in the PRPH2 disease cohort. We invoked ACMG criteria [PM2, BP4] and classified NM_000322.4:c.937C>T in the PRPH2 gene as a Variant of Uncertain Significance. |
Leiden Open Variation Database | RCV001530386 | SCV001745195 | uncertain significance | not provided | 2021-04-06 | no assertion criteria provided | curation | Curator: Global Variome, with Curator vacancy. Submitter to LOVD: Manon Peeters. |