Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003136496 | SCV003821259 | uncertain significance | not provided | 2020-11-20 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003358144 | SCV004080115 | uncertain significance | Inborn genetic diseases | 2023-08-02 | criteria provided, single submitter | clinical testing | The c.4930G>T (p.V1644L) alteration is located in exon 24 (coding exon 24) of the SCN4A gene. This alteration results from a G to T substitution at nucleotide position 4930, causing the valine (V) at amino acid position 1644 to be replaced by a leucine (L). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV005029913 | SCV005649632 | uncertain significance | Potassium-aggravated myotonia; Paramyotonia congenita of Von Eulenburg; Hypokalemic periodic paralysis, type 2; Hyperkalemic periodic paralysis; Congenital myasthenic syndrome 16; Congenital myopathy 22A, classic; Congenital myopathy 22B, severe fetal | 2024-06-12 | criteria provided, single submitter | clinical testing |