Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001544825 | SCV001764035 | uncertain significance | not provided | 2020-04-27 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis, which includes protein predictors and evolutionary conservation, supports a deleterious effect |
Fulgent Genetics, |
RCV005014584 | SCV005649631 | uncertain significance | Potassium-aggravated myotonia; Paramyotonia congenita of Von Eulenburg; Hypokalemic periodic paralysis, type 2; Hyperkalemic periodic paralysis; Congenital myasthenic syndrome 16; Congenital myopathy 22A, classic; Congenital myopathy 22B, severe fetal | 2024-02-21 | criteria provided, single submitter | clinical testing | |
Department of Neurology and Geriatrics, |
RCV002305614 | SCV002600049 | uncertain significance | Hypokalemic periodic paralysis, type 1 | 2022-04-12 | no assertion criteria provided | research |