Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Blueprint Genetics | RCV000208085 | SCV000264206 | uncertain significance | Primary dilated cardiomyopathy | 2015-07-06 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002399771 | SCV002704221 | uncertain significance | Cardiovascular phenotype | 2022-10-11 | criteria provided, single submitter | clinical testing | The p.H557Q variant (also known as c.1671C>G), located in coding exon 11 of the SCN5A gene, results from a C to G substitution at nucleotide position 1671. The histidine at codon 557 is replaced by glutamine, an amino acid with highly similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |