Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003540969 | SCV000946664 | uncertain significance | not provided | 2022-03-26 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs748732150, gnomAD 0.0009%). This sequence change replaces histidine, which is basic and polar, with asparagine, which is neutral and polar, at codon 588 of the SCN5A protein (p.His588Asn). This variant has not been reported in the literature in individuals affected with SCN5A-related conditions. ClinVar contains an entry for this variant (Variation ID: 651320). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The asparagine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV001841984 | SCV001347820 | likely benign | Cardiac arrhythmia | 2019-03-16 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV001841984 | SCV004825646 | uncertain significance | Cardiac arrhythmia | 2023-06-28 | criteria provided, single submitter | clinical testing |