Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
de |
RCV003492863 | SCV004022241 | likely pathogenic | Brugada syndrome 1; Long QT syndrome 3 | 2023-07-21 | no assertion criteria provided | research | The variant NM_000335.5:c.504C>A (chr3:38620950) in SCN5A was detected in 2 heterozygotes out of 58K WGS Icelanders (MAF= 0,002%). This variant has not been reported in ClinVar previously. Based on ACMG criteria (PVS1, PM2) this variant classifies as likely pathogenic. |