Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000664603 | SCV000788596 | uncertain significance | Dilated cardiomyopathy 1L; Autosomal recessive limb-girdle muscular dystrophy type 2F | 2017-04-27 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000814111 | SCV000954510 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2F | 2022-01-17 | criteria provided, single submitter | clinical testing | This sequence change affects the initiator methionine of the SGCD mRNA. The next in-frame methionine is located at codon 2. This variant is present in population databases (rs756367674, gnomAD 0.02%). This variant has not been reported in the literature in individuals affected with SGCD-related conditions. ClinVar contains an entry for this variant (Variation ID: 549998). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV000664603 | SCV002789252 | uncertain significance | Dilated cardiomyopathy 1L; Autosomal recessive limb-girdle muscular dystrophy type 2F | 2021-11-02 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000814111 | SCV003931749 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2F | 2023-02-08 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV003233796 | SCV003931750 | uncertain significance | Dilated cardiomyopathy 1L | 2023-02-08 | criteria provided, single submitter | clinical testing |