Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000808297 | SCV000948401 | uncertain significance | Lewy body dementia; Autosomal dominant Parkinson disease 1 | 2021-09-22 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 652694). This variant has not been reported in the literature in individuals affected with SNCA-related conditions. This variant is present in population databases (rs145138372, ExAC 0.01%). This sequence change replaces proline with threonine at codon 117 of the SNCA protein (p.Pro117Thr). The proline residue is moderately conserved and there is a small physicochemical difference between proline and threonine. |
Fulgent Genetics, |
RCV002478876 | SCV002783498 | uncertain significance | Lewy body dementia; Autosomal dominant Parkinson disease 1; Autosomal dominant Parkinson disease 4 | 2022-04-21 | criteria provided, single submitter | clinical testing |