Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Blueprint Genetics | RCV001073459 | SCV001239001 | likely pathogenic | Retinal dystrophy | 2019-02-27 | criteria provided, single submitter | clinical testing | |
Dept Of Ophthalmology, |
RCV001073459 | SCV004704835 | uncertain significance | Retinal dystrophy | 2023-10-01 | criteria provided, single submitter | research | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004587038 | SCV005076344 | uncertain significance | not specified | 2024-04-12 | criteria provided, single submitter | clinical testing | Variant summary: ABCA4 c.2791G>T (p.Val931Leu) results in a conservative amino acid change located in the ABC transporter-like, ATP-binding domain (IPR003439) of the encoded protein sequence. Four of five in-silico tools predict a benign effect of the variant on protein function. The variant was absent in 251362 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.2791G>T in individuals affected with Retinitis Pigmentosa and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 865894). Based on the evidence outlined above, the variant was classified as uncertain significance. |