Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001388592 | SCV001589645 | pathogenic | not provided | 2020-11-18 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in ABCA4 are known to be pathogenic (PMID: 10958761, 24938718, 25312043, 26780318). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may create or strengthen a splice site, but this prediction has not been confirmed by published transcriptional studies. This variant has been observed in individual(s) with clinical features of ABCA4-related conditions (PMID: 24713488). ClinVar contains an entry for this variant (Variation ID: 812200). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Tyr1723*) in the ABCA4 gene. It is expected to result in an absent or disrupted protein product. |
Sharon lab, |
RCV001002820 | SCV001160835 | pathogenic | Stargardt disease | 2019-06-23 | no assertion criteria provided | research |