Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001822660 | SCV002071840 | uncertain significance | not specified | 2021-08-31 | criteria provided, single submitter | clinical testing | DNA sequence analysis of the ABCC8 gene demonstrated a sequence change in intron 8, c.1332+9T>C. This change does not appear to have been previously described in patients with ABCC8-related disorders and has been described in the gnomAD database in three heterozygous individuals which corresponds to a population frequency of 0.0012% (dbSNP rs775059899). This sequence change is not clearly predicted to have a deleterious effect on splicing based on in silico splice prediction programs. The functional significance of this sequence change is not known at present and its contribution to this patient's disease phenotype cannot definitively be determined. |
Labcorp Genetics |
RCV002074363 | SCV002374187 | likely benign | not provided | 2023-11-07 | criteria provided, single submitter | clinical testing |