Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Pars Genome Lab | RCV001533220 | SCV001749016 | benign | Hyperinsulinemic hypoglycemia, familial, 1 | 2021-07-01 | criteria provided, single submitter | clinical testing | |
Pars Genome Lab | RCV001533221 | SCV001749017 | benign | Diabetes mellitus, transient neonatal, 2 | 2021-07-01 | criteria provided, single submitter | clinical testing | |
Pars Genome Lab | RCV001533222 | SCV001749018 | benign | Diabetes mellitus, permanent neonatal 3 | 2021-07-01 | criteria provided, single submitter | clinical testing | |
Pars Genome Lab | RCV001533282 | SCV001749098 | benign | Leucine-induced hypoglycemia | 2021-07-01 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001615250 | SCV001840311 | benign | not provided | 2018-08-09 | criteria provided, single submitter | clinical testing | |
Clinical Genomics, |
RCV002285176 | SCV002574774 | benign | Maturity onset diabetes mellitus in young | criteria provided, single submitter | research | Mutations in ABCC8 gene are associated with both neonatal diabetes mellitus as well as MODY. Patients with this mutation may have a better response to sulfonylureas. However, no sufficient evidence is found to ascertain the role of this particular variant ( rs4148632) in MODY yet. | |
Clinical Genomics, |
RCV002285177 | SCV002574775 | uncertain significance | Transitory neonatal diabetes mellitus | criteria provided, single submitter | research | Mutations in ABCC8 gene are associated with both neonatal diabetes mellitus as well as MODY. Patients with this mutation may have a better response to sulfonylureas. However, no sufficient evidence is found to ascertain the role of this particular variant (rs4148632) in neonatal diabetes yet. |