Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Myriad Genetics, |
RCV002310409 | SCV002602395 | likely pathogenic | Hyperinsulinemic hypoglycemia, familial, 1 | 2021-12-31 | criteria provided, single submitter | clinical testing | NM_000352.3(ABCC8):c.3842delG(G1281Afs*8) is expected to be pathogenic in the context of familial hyperinsulinism, ABCC8-related. This variant is predicted to lead to an abnormal or absent protein product due to the creation of a premature termination codon in ABCC8, a gene where loss-of-function variants are known to be pathogenic. Please note: this variant was assessed in the context of healthy population screening. |