Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001817965 | SCV002067504 | uncertain significance | not specified | 2020-06-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002386579 | SCV002693414 | uncertain significance | Inborn genetic diseases | 2021-08-16 | criteria provided, single submitter | clinical testing | The p.D325N variant (also known as c.973G>A), located in coding exon 6 of the ABCC8 gene, results from a G to A substitution at nucleotide position 973. The aspartic acid at codon 325 is replaced by asparagine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV002478065 | SCV002778831 | uncertain significance | Diabetes mellitus, transient neonatal, 2; Hyperinsulinemic hypoglycemia, familial, 1; Leucine-induced hypoglycemia; Type 2 diabetes mellitus; Diabetes mellitus, permanent neonatal 3 | 2021-11-02 | criteria provided, single submitter | clinical testing |