Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000463910 | SCV000552361 | likely pathogenic | Tuberous sclerosis 1 | 2016-10-13 | criteria provided, single submitter | clinical testing | In summary, donor and acceptor splice site variants are typically loss-of-function (PMID: 16199547), and loss-of-function variants in TSC1 are known to be pathogenic (PMID: 10227394, 17304050). However, without additional functional and/or genetic data, this variant has been classified as Likely Pathogenic. This variant has not been reported in the literature in individuals with a TSC1-related disease. This sequence change affects a donor splice site in intron 18 of the TSC1 gene. It is expected to disrupt RNA splicing and likely results in an absent or disrupted protein product. |