Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000525091 | SCV000641611 | likely benign | Tuberous sclerosis 1 | 2025-02-03 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002316554 | SCV000849887 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-08-04 | criteria provided, single submitter | clinical testing | The p.N1008S variant (also known as c.3023A>G), located in coding exon 21 of the TSC1 gene, results from an A to G substitution at nucleotide position 3023. The asparagine at codon 1008 is replaced by serine, an amino acid with highly similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Genome- |
RCV000525091 | SCV002040217 | uncertain significance | Tuberous sclerosis 1 | 2021-11-07 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003476284 | SCV004204416 | uncertain significance | Isolated focal cortical dysplasia type II | 2023-10-26 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV003999215 | SCV004816451 | uncertain significance | Tuberous sclerosis syndrome | 2023-12-01 | criteria provided, single submitter | clinical testing |