Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000690055 | SCV000817732 | likely benign | Tuberous sclerosis 1 | 2024-02-05 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003163141 | SCV003911758 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-12-04 | criteria provided, single submitter | clinical testing | The p.A1072V variant (also known as c.3215C>T), located in coding exon 21 of the TSC1 gene, results from a C to T substitution at nucleotide position 3215. The alanine at codon 1072 is replaced by valine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
All of Us Research Program, |
RCV003999538 | SCV004827486 | uncertain significance | Tuberous sclerosis syndrome | 2023-05-31 | criteria provided, single submitter | clinical testing |