Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001019167 | SCV001180490 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-04-01 | criteria provided, single submitter | clinical testing | The p.P311T variant (also known as c.931C>A), located in coding exon 8 of the TSC1 gene, results from a C to A substitution at nucleotide position 931. The proline at codon 311 is replaced by threonine, an amino acid with highly similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV001203395 | SCV001374558 | likely benign | Tuberous sclerosis 1 | 2023-05-22 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV001203395 | SCV002039409 | uncertain significance | Tuberous sclerosis 1 | 2021-11-07 | criteria provided, single submitter | clinical testing |