Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002240170 | SCV001208717 | uncertain significance | Ehlers-Danlos syndrome, classic type, 1 | 2019-12-31 | criteria provided, single submitter | clinical testing | This sequence change replaces alanine with glutamic acid at codon 929 of the COL5A2 protein (p.Ala929Glu). The alanine residue is highly conserved and there is a moderate physicochemical difference between alanine and glutamic acid. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals with COL5A2-related conditions. This variant is not present in population databases (ExAC no frequency). |