Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Refractive Surgery Department, |
RCV003324669 | SCV004030251 | likely pathogenic | Keratoconus | 2023-08-27 | no assertion criteria provided | clinical testing | In family 3, a heterozygous nonsynonymous mutation in exon 54 of COL5A2 (c.4364G>A, p.G1455E) was detected. This variant is also located in the COLFI domain, close to the C-terminal end (1265–1499 aa), within the fourth cross-linking site, which is predicted as being highly conserved among species and probably damaging. |