Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001564955 | SCV001788204 | pathogenic | not provided | 2021-06-21 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on NADPH oxidase activity (Beaumel S et al., 2014); In-frame deletion of 1 amino acids in a non-repeat region; Not observed at significant frequency in large population cohorts (Lek et al., 2016); In silico analysis supports a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 7579466, 20729109, 26210446, 9585602, 15693794, 15777347, 25252997, 27535533) |