Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Dunham Lab, |
RCV002305430 | SCV002599379 | pathogenic | Anemia, nonspherocytic hemolytic, due to G6PD deficiency | 2022-08-12 | criteria provided, single submitter | curation | Variant found in hemizygote with deficiency and CNSHA (PP4). Decreased activity in red blood cells (1%) (PS3). Affects same amino acid as pathogenic 410G>D (ClinVar ID 10398) (PM5). Within dimer interface (PM1). Predicted by PolyPhen and SIFT to be probably damaging and deleterious (PP3). Not found in gnomAD (PM2). Post_P 0.997 (odds of pathogenicity 3158, Prior_P 0.1). |
Revvity Omics, |
RCV002305430 | SCV004238194 | likely pathogenic | Anemia, nonspherocytic hemolytic, due to G6PD deficiency | 2023-08-14 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000011102 | SCV000031329 | other | G6PD RIVERSIDE | 2013-04-18 | no assertion criteria provided | literature only |