Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV002542537 | SCV005061671 | likely benign | Glanzmann thrombasthenia | 2024-04-16 | reviewed by expert panel | curation | The c.1210+8A>G variant is an intronic variant that is not predicted by SpliceAI to impact splicing. In addition, it occurs at a nucleotide that is not conserved as shown by phyloP score of -0.54 (BP4 and BP7). This variant was submitted to ClinVar in one patient with Glanzmann Thrombasthenia. After a thorough literature search, this variant was not found to be reported in any patients with Glanzmann Thrombasthenia. The highest population minor allele frequency in gnomAD v4.0.0 is 0.0006283 (47/74808 alleles) in the African/African American population. This intermediate allele frequency is lower than the ClinGen PD VCEP threshold (>0.00158) for BS1 but higher than the threshold (<0.0001) for PM2_Supporting. In summary, this variant meets the criteria to be classified as likely benign for autosomal recessive Glanzmann Thrombasthenia based on the ACMG/AMP criteria applied, as specified by the ClinGen PD VCEP: BP4, BP7. (VCEP specifications version 2; date of approval xx/xx/xxxx) |
Genetic Services Laboratory, |
RCV001817485 | SCV002068372 | uncertain significance | not specified | 2019-10-24 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002542537 | SCV003251447 | likely benign | Glanzmann thrombasthenia | 2023-12-06 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004552040 | SCV004779440 | likely benign | ITGA2B-related disorder | 2021-02-09 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |