Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340755 | SCV004047451 | uncertain significance | Platelet-type bleeding disorder 16 | criteria provided, single submitter | clinical testing | The missense variant c.2320C>T (p.Arg774Trp) in ITGA2B gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Arg774Trp variant is novel (not in any individuals) in 1000 Genomes and allele frequency of 0.00003182% is reported in gnomAD. The amino acid Arg at position 774 is changed to a Trp changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Arg774Trp in ITGA2B is predicted as conserved by PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |