Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV001290466 | SCV001478502 | uncertain significance | Glanzmann thrombasthenia | 2024-03-07 | reviewed by expert panel | curation | The NM_000419.5(ITGA2B):c.68C>A (p.Pro23His) missense variant has been reported in at least one compound heterozygous GT proband (ASH poster abstract only: doi.org/10.1182/blood.V110.11.3921.3921). The variant is absent from all population database cohorts, including gnomADv4.0 (PM2_supporting). In summary this variant meets criteria to be classified as uncertain significance for GT. GT-specific criteria applied: PM2_Supporting. |