Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002606420 | SCV003498580 | uncertain significance | Glanzmann thrombasthenia | 2023-04-06 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 2181978). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant  is likely to be tolerated. This variant has not been reported in the literature in individuals affected with ITGA2B-related conditions. This variant is present in population databases (rs531610168, gnomAD 0.03%). This sequence change replaces alanine, which is neutral and non-polar, with threonine, which is neutral and polar, at codon 297 of the ITGA2B protein (p.Ala297Thr). |