Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV001125285 | SCV004037415 | uncertain significance | Glanzmann thrombasthenia | 2023-09-07 | reviewed by expert panel | curation | The c.964C>T variant in ITGA2B is a missense variant predicted to cause substitution of Histidine by Tyrosine at amino acid 322 (p.His322Tyr). This variant is absent from gnomAD v2.1.1 (PM2_Supporting). This variant was observed as part of a predisposition screen in an ostensibly healthy population by Illumina. In summary, this variant meets the criteria to be classified as Uncertain significance - insufficient evidence for autosomal recessive Glanzmann Thrombasthenia based on the ACMG/AMP criteria applied, as specified by the ClinGen PD VCEP: PM2_Supporting (VCEP specifications version 2). |
Illumina Laboratory Services, |
RCV001125285 | SCV001284333 | uncertain significance | Glanzmann thrombasthenia | 2017-04-27 | criteria provided, single submitter | clinical testing | This variant was observed as part of a predisposition screen in an ostensibly healthy population. A literature search was performed for the gene, cDNA change, and amino acid change (where applicable). No publications were found based on this search. Allele frequency data from public databases did not allow this variant to be ruled in or out of causing disease. Therefore, this variant is classified as a variant of unknown significance. |