Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000519160 | SCV000620756 | uncertain significance | not provided | 2017-09-13 | criteria provided, single submitter | clinical testing | The L685P variant has been previously reported as a polymorphism with a frequency of 2.4% (Tezak et al., 2003). However, the L685P variant is not observed in large population cohorts (Lek et al., 2016). This variant is a semi-conservative amino acid substitution, which may impact secondary protein structure as these residues differ in some properties. This substitution occurs at a position that is conserved across species, and in silico analysis predicts this variant is probably damaging to the protein structure/function. |
Biochemical Molecular Genetic Laboratory, |
RCV000985077 | SCV001133035 | likely pathogenic | Merosin deficient congenital muscular dystrophy | 2019-09-26 | no assertion criteria provided | clinical testing |