Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003134718 | SCV003816561 | uncertain significance | Succinyl-CoA acetoacetate transferase deficiency | 2022-05-30 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003274336 | SCV003955316 | uncertain significance | Inborn genetic diseases | 2023-06-06 | criteria provided, single submitter | clinical testing | The c.863G>C (p.G288A) alteration is located in exon 9 (coding exon 9) of the OXCT1 gene. This alteration results from a G to C substitution at nucleotide position 863, causing the glycine (G) at amino acid position 288 to be replaced by an alanine (A). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |