Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Precision Medicine Center, |
RCV001375678 | SCV001572598 | pathogenic | Autosomal recessive nonsyndromic hearing loss 4 | criteria provided, single submitter | research | PVS1: Null variant in the gene with established LOF as a disease mechanism PM2: not found in gnomAD PM3: Pathogenic mutation confirmed in trans in one patient PP4: Patient's phenotype highly specific for gene |