Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Columbia University Laboratory of Personalized Genomic Medicine, |
RCV000853537 | SCV000994920 | likely pathogenic | Amyotrophic lateral sclerosis type 1 | 2014-03-20 | criteria provided, single submitter | clinical testing | It is noteworthy that compound heterozygous variants D90A and D96N (HGVS: new numbering, D97N)located in the same protein domain have been previously described in a recessive ALS family (Hand et al. Ann Neurol 2001:49;267-271) suggesting that the D97V variant is likely pathogenic and associated with autosomal recessive ALS. The D97V variant was detected through WES analysis in the blood leukocytes of a healthy 73-year-old male control subject with no family history of ALS (four older siblings with no known neuromuscular disorders). |