Total submissions: 8
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000411127 | SCV000489599 | likely benign | Peutz-Jeghers syndrome | 2016-10-25 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000583250 | SCV000691473 | likely benign | Hereditary cancer-predisposing syndrome | 2016-08-18 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001718802 | SCV000729554 | likely benign | not provided | 2020-02-25 | criteria provided, single submitter | clinical testing | |
Invitae | RCV000411127 | SCV002470656 | likely benign | Peutz-Jeghers syndrome | 2024-01-05 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000583250 | SCV002531634 | benign | Hereditary cancer-predisposing syndrome | 2021-05-05 | criteria provided, single submitter | curation | |
Myriad Genetics, |
RCV000411127 | SCV004017938 | likely benign | Peutz-Jeghers syndrome | 2023-04-12 | criteria provided, single submitter | clinical testing | This variant is considered likely benign. This variant is intronic and is not expected to impact mRNA splicing. |
All of Us Research Program, |
RCV000411127 | SCV004821571 | likely benign | Peutz-Jeghers syndrome | 2023-12-18 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV000411127 | SCV001550396 | likely benign | Peutz-Jeghers syndrome | no assertion criteria provided | clinical testing | The STK11 c.1109-13G>A variant was not identified in the literature nor was it identified in the Cosmic, LOVD 3.0, Zhejiang University, or Insight Hereditary Tumors databases. The variant was identified in dbSNP (ID: rs568152768) as "With Likely benign allele” and ClinVar (classified as likely benign by Counsyl, GeneDx, and Color Genomics). The variant was identified in control databases in 16 of 264868 chromosomes at a frequency of 0.00006 (Genome Aggregation Database Feb 27, 2017). The variant was observed in the following populations: East Asian in 13 of 18550 chromosomes (freq: 0.0007), Other in 1 of 6206 chromosomes (freq: 0.0001), and South Asian in 2 of 29794 chromosomes (freq: 0.000067); it was not observed in the African, Latino, European, Ashkenazi Jewish, or Finnish, populations. The variant occurs outside of the splicing consensus sequence and in silico or computational prediction software programs (SpliceSiteFinder, MaxEntScan, NNSPLICE, GeneSplicer) do not predict a difference in splicing. In summary, based on the above information, the clinical significance of this variant cannot be determined with certainty at this time although we would lean towards a more benign role for this variant. This variant is classified as likely benign. |