Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000792286 | SCV000931572 | uncertain significance | Peutz-Jeghers syndrome | 2023-01-06 | criteria provided, single submitter | clinical testing | This sequence change replaces proline, which is neutral and non-polar, with arginine, which is basic and polar, at codon 38 of the STK11 protein (p.Pro38Arg). This variant is not present in population databases (gnomAD no frequency). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt STK11 protein function. ClinVar contains an entry for this variant (Variation ID: 639482). This variant has not been reported in the literature in individuals affected with STK11-related conditions. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001805858 | SCV002051317 | uncertain significance | not specified | 2021-12-22 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000792286 | SCV002057738 | uncertain significance | Peutz-Jeghers syndrome | 2021-07-15 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV000792286 | SCV004827189 | uncertain significance | Peutz-Jeghers syndrome | 2023-12-01 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV004569504 | SCV005052887 | uncertain significance | Melanoma, cutaneous malignant, susceptibility to, 1 | 2023-12-28 | criteria provided, single submitter | clinical testing |