Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001389317 | SCV001590639 | pathogenic | Peutz-Jeghers syndrome | 2024-01-05 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln112*) in the STK11 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in STK11 are known to be pathogenic (PMID: 15188174, 16287113). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with clinical features of Peutz-Jeghers syndrome (PMID: 17404884, 26979979, 30334930). ClinVar contains an entry for this variant (Variation ID: 1075653). For these reasons, this variant has been classified as Pathogenic. |
Myriad Genetics, |
RCV001389317 | SCV004933169 | pathogenic | Peutz-Jeghers syndrome | 2024-02-12 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |