Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000474445 | SCV000541125 | uncertain significance | Peutz-Jeghers syndrome | 2023-10-06 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 3 of the STK11 gene. It does not directly change the encoded amino acid sequence of the STK11 protein. It affects a nucleotide within the consensus splice site. This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with STK11-related conditions. ClinVar contains an entry for this variant (Variation ID: 403768). Variants that disrupt the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). RNA analysis performed to evaluate the impact of this variant on mRNA splicing indicates it does not significantly alter splicing (Invitae). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV000581483 | SCV000691506 | likely benign | Hereditary cancer-predisposing syndrome | 2017-06-08 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000474445 | SCV000786207 | uncertain significance | Peutz-Jeghers syndrome | 2018-03-20 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000581483 | SCV001184611 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-03-01 | criteria provided, single submitter | clinical testing | The c.464+3G>A intronic variant results from a G to A substitution 3 nucleotides after coding exon 3 in the STK11 gene. This nucleotide position is poorly conserved in available vertebrate species. In silico splice site analysis predicts that this alteration will not have any significant effect on splicing. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Genome- |
RCV000474445 | SCV002057243 | uncertain significance | Peutz-Jeghers syndrome | 2021-07-15 | criteria provided, single submitter | clinical testing | |
Myriad Genetics, |
RCV000474445 | SCV004017950 | likely benign | Peutz-Jeghers syndrome | 2023-04-12 | criteria provided, single submitter | clinical testing | This variant is considered likely benign. This variant is intronic and is not expected to impact mRNA splicing. |
All of Us Research Program, |
RCV000474445 | SCV004828575 | likely benign | Peutz-Jeghers syndrome | 2023-09-04 | criteria provided, single submitter | clinical testing |