Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001972514 | SCV002240509 | pathogenic | Peutz-Jeghers syndrome | 2021-09-26 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This premature translational stop signal has been observed in individual(s) with Peutz-Jeghers syndrome (PMID: 30334930). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Leu164Argfs*7) in the STK11 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in STK11 are known to be pathogenic (PMID: 15188174, 16287113). |