Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV000196256 | SCV000253696 | likely pathogenic | Peutz-Jeghers syndrome | 2015-05-02 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Likely Pathogenic. Truncating variants in STK11 are known to be pathogenic. This particular truncation has been reported in the literature (PMID: 20616022). This sequence change affects an acceptor splice site in intron 6. It is expected to disrupt mRNA splicing and likely results in an absent or disrupted protein product. |