Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002408309 | SCV002718187 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-06-28 | criteria provided, single submitter | clinical testing | The c.1904-2_1904-1delAG intronic variant, located in intron 9 of the BARD1 gene, results from a deletion of two nucleotides within intron 9 of the BARD1 gene. Alterations that disrupt the canonical splice site are expected to result in aberrant splicing. This nucleotide region is highly conserved in available vertebrate species. In silico splice site analysis predicts that this alteration will weaken the native splice acceptor site and will result in the creation or strengthening of a novel splice acceptor site. The resulting transcript is predicted to be in-frame and is not expected to trigger nonsense-mediated mRNAdecay; however, direct evidence is unavailable. The exact functional effect of the altered amino acid sequence is unknown. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Laboratory for Genotyping Development, |
RCV003164546 | SCV002758369 | pathogenic | Gastric cancer | 2021-07-01 | no assertion criteria provided | research |