Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV003441722 | SCV004170213 | pathogenic | not provided | 2023-09-30 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); Canonical splice site variant predicted to result in a null allele in a gene for which loss of function is a known mechanism of disease; Published functional studies demonstrate a damaging effect, specifically ligation of the exon 6 and 7 sequences (Ruffner et al., 1988); This variant is associated with the following publications: (PMID: 3353369, 22227324, 32553838) |
OMIM | RCV000019869 | SCV000040167 | pathogenic | Analbuminemia | 1988-04-01 | no assertion criteria provided | literature only |