Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV000266690 | SCV000354300 | benign | Hypophosphatasia | 2018-01-13 | criteria provided, single submitter | clinical testing | This variant was observed in the ICSL laboratory as part of a predisposition screen in an ostensibly healthy population. It had not been previously curated by ICSL or reported in the Human Gene Mutation Database (HGMD: prior to June 1st, 2018), and was therefore a candidate for classification through an automated scoring system. Utilizing variant allele frequency, disease prevalence and penetrance estimates, and inheritance mode, an automated score was calculated to assess if this variant is too frequent to cause the disease. Based on the score and internal cut-off values, a variant classified as benign is not then subjected to further curation. The score for this variant resulted in a classification of benign for this disease. |
ARUP Laboratories, |
RCV000756986 | SCV000884997 | likely benign | not provided | 2018-03-04 | criteria provided, single submitter | clinical testing | The c.534C>T; p.Tyr178Tyr variant (rs201250289) does not alter the amino acid sequence of the ALPL protein and computational splice site prediction algorithms do not predict a change in the nearest splice site or creation of a cryptic splice site. This variant has not been reported in medical literature or in gene specific variation databases. This variant is listed in the genome Aggregation Database (gnomAD) with an East Asian population frequency of 0.47% (identified on 88 out of 18,866 chromosomes, including one homozygote), and is classified as likely benign in ClinVar (ID: 295544). Based on the available information, the c.534C>T variant is likely to be benign. |
Labcorp Genetics |
RCV000756986 | SCV001048666 | benign | not provided | 2024-01-31 | criteria provided, single submitter | clinical testing |