Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
CSER _CC_NCGL, |
RCV000019654 | SCV000190627 | uncertain significance | Hereditary antithrombin deficiency | 2014-06-01 | criteria provided, single submitter | research | Low GERP score may suggest that this variant may belong in a lower pathogenicity class |
Fulgent Genetics, |
RCV000019654 | SCV002800940 | uncertain significance | Hereditary antithrombin deficiency | 2021-11-04 | criteria provided, single submitter | clinical testing | |
Gene |
RCV005051736 | SCV005685592 | uncertain significance | not provided | 2024-07-22 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 25637381, 24055113, 1483709) |
OMIM | RCV000019654 | SCV000039952 | pathogenic | Hereditary antithrombin deficiency | 1992-12-01 | no assertion criteria provided | literature only |